Abstract: Escobar (multiple pterygium) syndrome is a rare autosomal ... We report a case of multiple pterygium syndrome most likely the first reported case in Thailand that still .... Renal Ultrasound ... or lethal pterygium condition, during genetic.
Multiple PterygiumSyDdmme (EscobarSyndrome)
Report of a Casewith Surgical Correction and Review of Literaturc Porn\sanWasrnt,ll.D.,' Kondpom Kaeypons*$r M D.** Monrri Knnrnee. M.D.''
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Ttc mulriplc ptrycium syndrcEc*s &$ by codio et al io 1e76ro rcpon in described
l o d g l . ' m o u l c o m eo l : u r g i c a o d
lndsp.utic
CASD R.EPORT skitr*.bl (p'crycia) onsenihl irttuosryposjs, rcms Fi6 ,J'n m nrusFr hci*. siinila phemrypeswerc prvioary r.pon.d by BuRsicrc(te02) md Mdddy (e36), thc udrdns jndudedpdsis mdm41!nyhidicppedcl'jldrcnwAadniudb cddics Uiil' Depillm4t of Pcdfutics,sifiaj
idercruEl rcs. Also trotn wcic syddacrylyand
bolheye|i{alilidoigoloiddaniofth.pal0chdl
scdbr rnomalnsud numqotrsjoiDt otrrEcruK, d*nl,cd in $c wond litsdrc uidei rhc diasn(s ofdhmgyPosismdlpl.xMg6ib'It'sjoh$itd in an atr'osomd'46sive mon.r.Tbe phenotpic
.quimvarusdcroniry ad sli6is. (r,strc t,2) ller heishl weisnt od h.ad ciKunr.rtrcc wcre pcrr bclow third pdedile. sh. hd doft,r iorcllic.ic. orlH pcs ivc physiol fiidinge in.lndc
(') e{msive pr'ysia rrcs rhe mjor Fha p) nqq 6ihdr6 (:r) reo'iosk (4) crefrpftb (s) prcis (6) turiFs cquinovins (7) shod satorc ard (lt) rulriple nircr lEill ,ionali.s. Limb prerysir Mcor m i compdicnt or at l*r
r dves 3yndsnc N norcdby ltull er al in
m{hr erch (DDsr) rinsuse 3 yr 5 m'r's(&morosi€r as : 3 ya 5 mrhtj Emr drsddei,phy dioi (h*dry)
pdiunt. tlowev.r,funhd $udy m rccdM to dcrcmiie [r. expcc'ricy, sociil dju$n.d aid
mmir :oipnbiizcd bmosim
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ch6t and hdd deromity, bilatemlblip* eqdnovaru deromrv a. rcrd
TsbL 1. C.n@ftotr ol ohdoiypic re{urs ar ou patieit ,id orhd rponc
i@k, uilli.,
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poplitcd
onbopediG,plaiic pbysiel medicine&
nek, sille,
.lbos
and k!@
Mu'dph Pb4ltUD sFtune
(r 7 r4 md curedidr
DISCUSSION ddemsr d,he ioitr' wi'h $beqEddcvdopnqr
CONCLUSION Mulriph Pbrysinm(Escobr)syidrcmcis !
2. s.oliosh usuilly dsvcloF hddr. 5 yctrs
p'imry ciE
physichn or |]c lilticili.
.nhopcdisr,
i^ miori'y of cs$
dosling'Ultrlsmqmphy
in*sk
ni,joily dt,hsc rcqrLired $rgsy or F icd *s
join, novemcd &d m6dc srsgrh
ACKNOWLEDGEMENT
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r-ni,ns M.nfirr (Fnl.mi) M..i:&J, m:.u
Unit for cridias daluttion, n ,.ins wiludio. .nd NUF
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