Supplemental Table S1 - Disease Models & Mechanisms

Supplemental table S1. Primers used in quantitative real-time polymerase chain reaction Primer name Human NDUFA9 Human NDUFB6 Human NDUFS3 Human MTND1 Human MTND2 Human MTND4 Human MTND4L Human MTND6 Human β-actin Human GADPH Human UQCRC1 Human UQCRC2 Human UQCRFS Human MTCYB Human SDHA Human COX4 Human MTCO1 Human ATP5A1 Human MTATP6 Human iNOS Human CYP2E1 Human xanthine oxidase (XDH) Human NOX4 Human NOX2 Human p47phox Human p22phox Human RAC1

Direction Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense Sense Antisense

Sequence 5′-GAT TGT 5′-CTC CAG 5′-CTG CAG 5′-GAA TAA 5′-GTC AGA 5′-CTC AAA

GGC CTT CAG TCC CCA ACG

CAC CCT CTG AGA CGG GTT

TGT TGG CGA CAG AAT TTG

GTT TGG-3′ ACA GT-3 GA-3′ GTA CAA G-3′ GAT GTG-3′ CCG AG-3′

5’-CTT AGC TCT CAC CAT CGC TCT T-3’ 5’-AGA TTG TTT GGG CTA CTG CTC G-3’ 5’-CTT AGC ATA CTC CTC AAT TAC CCA-3’ 5’-TGG ATG GAA TTA AGG GTG TTA GTC-3’ 5’-CTC 5’-TGA 5’-GCA 5’-GTT

CAC TTG TTT GGA

TTA AAG ACC GAT

TGA AGT ATC TGA

CTC ATG TCA GAC

CCT CAA CTT TAG

AAA TGA CTA TAG

G-3’ GCG-3’ GG-3’ G-3’

5’-ATC 5’-GAT 5’-GGA 5’-GTA 5’-GCC 5’-ATG 5′-GTT 5′-CTT 5′-CCA 5′-CAT 5′-GCC 5′-CTG

CTC GGT CGA GAT AAA GAT AGC GAT AAT TAG TGT GAA

CCG TGT CAT GGG AGG GAC CTG GTA GGC AAT GTT ACG

AAT CTT GGA CAC GTC CTT CTG GTA TTG ATC GGA AAC

CAA TGG GAA AGT ATC GGC GAC AGC GTG AAC CCT TGG

CCC TG-3 ATA TA-3’ AAT CTG GCA-3’ GTG GGT G-3’ ATC T-3’ CAG-3’ AAC G-3′ TGT GTG C-3 ATT GC-3′ ATC ACC CC-3 GAA G-3′ GTG AC-3

5’-GAT 5’-GGA 5′-GGC 5′-GTT 5′-CAG 5′-CTC

CCT GGA TTG CTG GGT CTT

CCA TAA CGA CTA ATT GAA

AAT TGC GCT AAC TAG CTT

CAC CGA GCA GGC CCT AAT

CAC TGT TTT ATG AGT GCG

AGG AC-3’ TTC AG-3’ GG-3′ CCA-3′ TGG-3′ ATA C-3′

5’-GAG CTG GGC CAG CCA GGC AA-3’ 5’-GGA AAC GCC ATA TCG GGG GCA-3’ 5’-GTA TTG GTG ATG GTA TTG CCC GC-3’ 5’-AAC AGC TCC TCA CCA ACT GGA AC-3’ 5’-GGC TTTC GCT CTA AGA TTA AAA ATG-3’ 5’-GTA GAG GGA AGG TTA ATG TG-3’ 5’-TGT TTG AAC ACA TCT GCA GAC ACG-3’ 5’-CAA GGT CAG GTG GGA TTT CGA AGA-3’ 5’-GCC TAC GAC TGT TGT GAA CAC TG-3’ 5’-CAA GAG GCT GCT GCG TCT GCA-3’ 5’-CTG AGG CTG AAA GAC ACT CCT C-3’ 5’-GAA GCT TAG CAA CAG CAT CCA CC-3’ 5’-CTT CTC TTC ACA ACT GTT CCT GGC-3’ 5’-GAG CTG GTT CGG TTA AGA CTG ATG-3’ 5’-GAG TTT CAA GAT GCG TGG AAA CT-3’ 5’-AGA TCT GCA AAC CAC TCA AAG G-3’ 5’-CCG AGA TCT ACG AGT TCC AT-3’ 5’-GAG CTT GAG GTC ATC AGG G-3’ 5’-TTT GTG TGC CTG CTG GAG T-3’ 5’-AGT GGA TAG ATG CCG CTC G-3’ 5’-GTG AAT CTG GGC TTA TGG GAT-3’ 5’-GTG ATG GGA GTC AGC TTC TT-3’

Disease Models & Mechanisms | Supplementary Material