Von Willebrand factor-cleaving protease - CiteSeerX

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brand factor-cleaving protease (ADAMTS-13) ac- tivity (
Original article

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Peer reviewed article

Von Willebrand factor-cleaving protease (ADAMTS-13) activity in thrombotic microangiopathies: diagnostic experience 2001/2002 of a single research laboratory J.-D. Studt a, J. A. Kremer Hovinga a, L. Alberioa, V. Bianchi b, B. Lämmlea (with contributions by P. Hénon c, E. Siebke d and M. Hermann e) a b c d e

Central Haematology Laboratory, Inselspital, University of Bern, Bern, Switzerland Present address: Clinica Medica, Ospedale Regionale di Lugano Département d’ Hématologie, Centre Hospitalier, Mulhouse, France Department of Pediatrics, Sentralsjukehuset, Ålesund, Norway University Children’s Hospital, Tübingen, Germany

Summary

The first two authors, J.-D. Studt and J. A. Kremer Hovinga, contributed equally to the study.

This work was supported by a grant from the Swiss National Foundation for Scientific Research (32–66756.01).

Background: Severe deficiency of von Willebrand factor-cleaving protease (ADAMTS-13) activity (