Introduction Case Report Discussion. References ...

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Vallecular cyst : A rare cause of Respiratory Distress and Stridor in. New Born. Saurabh Patel M.D.. 1. , Ankita Shukla, M.D.. 1. , Shardha Polam, M.D.. 1,2.
Vallecular cyst : A rare cause of Respiratory Distress and Stridor in New Born. 1 M.D. ,

1 M.D.

1,2 M.D.

Saurabh Patel Ankita Shukla, , Shardha Polam, 1 Department of Pediatrics , The Children’s Hospital at Saint Peter’s University Hospital, 2 Drexel University College of Medicine , New Brunswick, NJ

Introduction

Case Report

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A Vallecular cyst (VC) is a rare cause of stridor with or without respiratory distress in infants more commonly seen in adults Also known as retention cyst, epiglottic cyst, ductal cyst and base of tongue cyst. Increased risk of sudden respiratory distress and death May present from 1st week to 16th week of life

Radiology

41 week female infant 25 y ear old G1P0 ,NSVD, , B+/B+ maternal serologies negative  APGAR scores of 5 & 7 at age 1 & 5 mins Meconium stained AF Born apneic, and floppy at birth

Required intubation and suction below cords x 2 Transferred to ICN on ventillator Surfactant given X 1. ECHO obtained and infant started on pressor support d/t depressed cardiac funtion

CXR- small pneumothorax and pneumomediastinum- resolved without intervention Weaned gradually from ventilator on DOL 4 MRI brain/neck obtained for continued respiratory distress and increased FiO2 requirement- VALLECULAR CYST found as an incidental finding

ENT consulted. Pt tatken to OR and malsupialisation done. Respiratory Distress resolved. Fig 1 : sagital and coronal section depicting the vallecular cyst at the level of C2-C3

Discussion. VALLECULAR CYST can be fatal when associated with sudden airway obstruction Cyst forms as a consequence of either ductal obstruction of 1 mucous glands and or an embryological malformation . Bimodal age of presentation. Three major categories (based on adult observation): Ductal cysts (most common type) Thyroid cartilage foraminal cyst Saccular cysts Newborns can present with:2 Stridor Hoarse cry Feeding problems Chest retraction Apnea/cyanosis Failure to thrive Histology: contains respiratory epithelium with mucous glands. Diagnosis: Antenatal ultrasound and fetal MRI. Awake flexible laryngoscopy. Lateral X-ray of neck- difficult to interpret, but may be helpful. Treatment: Cyst Marsupialisation

References. Gutierrez JP, Berkowitz RG, Roberson CF. Vallecular cyst in Newborns and young infants.Pediatric Pulmonology 27:282-285 (1999). Hsieh WS, Yang PH, Wong KS, Li HY, Wang ECR, Yeh TF. Vallecular cyst: an uncommon cause of stridor in newborn infants. European Journal of Pediatrics. 159:79-81 (2000).